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1.
Rev. cuba. estomatol ; 58(4)dic. 2021.
Artigo em Espanhol | LILACS, CUMED | ID: biblio-1408361

RESUMO

Introducción: El tumor tritón maligno es una neoplasia rara en la que se encuentran células rabdomioblásticas en un tumor maligno de la vaina de nervios periféricos, que se caracteriza por su agresividad y mal pronóstico. La localización en la cabeza y el cuello es poco frecuente. La inmunohistoquímica juega un papel importante en el diagnóstico. Objetivo: Describir un tumor tritón maligno de tamaño inusual. Presentación del caso: Paciente femenino, de 16 años, es referida al servicio de cirugía maxilofacial del Instituto Nacional de Pediatría, Ciudad de México, con un diagnóstico de tumor neuroectodérmico en región facial y cervical de un año de evolución. Clínicamente el tumor era exofítico, multilobulado, con zonas extensas de necrosis, superficie de varias tonalidades y un tamaño aproximado de 18 x 10 x 12 cm. Se realizó una biopsia e inmunohistoquímica que confirmó el diagnóstico de tumor tritón maligno. La paciente fue intervenida quirúrgicamente, procedimiento con el cual se eliminó totalmente la lesión, con márgenes de seguridad. La paciente presentó una evolución tórpida, con desenlace fatal al cabo de seis meses del tratamiento. Conclusiones: El tumor tritón es una neoplasia agresiva y su detección oportuna orienta al cirujano a ofrecer al paciente un tratamiento adecuado(AU)


Introduction: Malignant triton tumor is a rare neoplasm in which rhabdomyoblasts are present in a malignant tumor of the peripheral nerve sheath. This condition is characterized by its aggressiveness and bad prognosis. Location in the head and neck is infrequent. Immunohistochemical testing plays an important role in its diagnosis. Objective: Describe an unusually large malignant triton tumor. Case presentation: A case is presented of a female 16-year-old patient referred to the maxillofacial surgery service of the National Institute of Pediatrics in Mexico City with a diagnosis of neuroectodermal tumor of one year's evolution in the facial and cervical region. In clinical terms, the tumor was exophytic, multilobed, with extensive areas of necrosis, a surface in several shades of color and an approximate size of 18 x 10 x 12 cm. Biopsy and immunohistochemical testing confirmed the diagnosis of malignant triton tumor. The patient underwent surgery in which the lesion was totally excised with a safety margin. Evolution was clumsy, with a fatal outcome at six months of treatment. Conclusions: Triton tumor is an aggressive neoplasm whose early detection makes it possible for surgeons to provide an appropriate treatment(AU)


Assuntos
Humanos , Cirurgia Bucal , Biópsia , Tumores Neuroectodérmicos/etiologia , Evolução Fatal , Seleção de Sítio de Tratamento de Resíduos
2.
Rev. odontopediatr. latinoam ; 11(2): 320197, 2021. tab, ilus
Artigo em Espanhol | LILACS, COLNAL | ID: biblio-1418996

RESUMO

En la actualidad, los bifosfonatos son utilizados en la población pediátrica con diagnóstico de osteogénesis imperfecta, desórdenes neuromusculares, displasia ósea, displasia fibrosa, osteoporosis idiopática juvenil, enfermedad de Crohn y trastornos reumatológicos. La osteonecrosis de los maxilares secundaria al tratamiento con bifosfonatos, se ha convertido en una complicación cada vez más común debido al incremento de su uso en la población adulta. En cuanto a la atención pediátrica la información es escasa. Este estudio presenta el caso clínico de una paciente de sexo femenino con diagnóstico de osteogénesis imperfecta tipo III quien fue tratada con múltiples extracciones dentales bajo anestesia general, previa Bifosfonatos en Odontopediatría: Revisión de la literatura, protocolo de manejo y reporte de un caso clínico Ingrid Báez Madrigal,1..... Rubí López Fernández,2..... Jorge Pedro Téllez Rodríguez,2..... Revista de Odontopediatría Latinoamericana¹ Estomatóloga Pediatra Egresada del Instituto Nacional de Pediatría.2Cirujano Maxilofacial, adscrito al Servicio de Estomatología del Instituto Nacional de Pediatría.Casos ClínicosDOI: 10.47990/alop.v11i2.278administración de amoxicilina 50 mg/kg 1 hora antes; debido a erupción anómala de caninos y primeros premolares superiores, así como persistencia de caninos y molares primarios superiores. Se realizaron citas control postoperatorias, en donde mostró adecuado proceso de cicatrización sin datos de necrosis maxilar. El objetivo es informar al estomatólogo sobre cómo actúan los bifosfonatos, los diagnósticos en la población pediátrica tratados con dicho fármaco y dar a conocer el protocolo de manejo de estos pacientes. Se realizó una revisión integradora en las bases de datos PubMed y Cochrane Library, los artículos fueron seleccionados de acuerdo a los criterios establecidos


Atualmente, os bisfosfonatos são utilizados na população pediátrica diagnosticada com osteogênese imperfeita, distúrbios neuromusculares, displasia óssea, displasia fibrosa, osteoporose idiopática juvenil, doença de Crohn e distúrbios reumatológicos. A osteonecrose dos maxilares secundárias ao tratamento com bifosfonatos tornou-se uma complicação cada vez mais comum devido ao aumento do uso na população adulta. Quanto ao atendimento pediátrico, as informações são escassas. Este estudo apresenta o caso clínico de uma paciente do sexo feminino com diagnóstico de osteogênese imperfeita tipo III, tratada com múltiplas exodontias sob anestesia geral, após administração de amoxicilina 50 mg / kg 1 hora antes; devido à erupção anômala de caninos superiores e primeiros pré-molares, bem como persistência de caninos decíduos superiores e molares. Foram marcadas consultas de controle pós-operatório, onde apresentava processo de cicatrização adequado, sem dados de necrose maxilar. O objetivo é informar ao estomatologista como os bisfosfonatos atuam, os diagnósticos na população pediátrica tratada com esse medicamento e apresentar o protocolo de manejo desses pacientes. Realizou-se revisão integrativa nas bases de dados PubMed e Cochrane Library, os artigos foram selecionados de acordo com os critérios estabelecidos


Bisphosphonates are currently used in the pediatric population diagnosed with osteogenesis imperfecta, neuromuscular disorders, skeletal dysplasia, fibrous dysplasia, juvenile idiopathic osteoporosis, Crohn's disease, and rheumatologic disorders.Bisphosphonate-related osteonecrosis of the jaw has become an increasingly common complication due to its increased use in the adult population. Regarding pediatric care, information is scarce. This study presents the clinical case of a female patient diagnosed with type III osteogenesis imperfecta who was treated with multiple dental extractions under general anesthesia, after administration of amoxicillin 50 mg/kg 1 hour before; due to anomalous eruption of upper canines and first premolars, as well as persistence of upper primary canines and molars. Postoperative control appointments were made, where she showed an adequate healing process without evidence of maxillary necrosis. The aim is to inform the stomatologist about how bisphosphonates act, the diagnoses in the pediatric population treated with


Assuntos
Humanos , Feminino , Difosfonatos , Osteogênese , Doença de Crohn , Anestesia
3.
Rev. esp. cir. oral maxilofac ; 41(4): 197-201, oct.-dic. 2019. ilus, tab
Artigo em Espanhol | IBECS | ID: ibc-191807

RESUMO

La signatia es una rara malformación congénita en la que se encuentra una fusión ósea del maxilar con la mandíbula. Puede ser unilateral o completa y se caracteriza por la incapacidad de abrir la boca del recién nacido. Esta puede clasificarse de acuerdo con su presentación clínica. Las complicaciones de esta anomalía pueden ser muy graves: incompatibilidad con la vida, incapacidad de proteger la vía aérea, dificultades para la alimentación, así como alteraciones en el crecimiento. Se han referido casos con distintos abordajes, por lo que el protocolo terapéutico-quirúrgico estará dado según las particularidades de cada individuo. En el presente caso se hace referencia de un lactante femenino que se presentó con fusión del complejo cigomático-maxilar con la mandíbula unilateral, el abordaje y seguimiento


Syngnathia is a rare congenital malformation in which a fusion of the mandible with the maxilla is found, it can be unilateral or complete and is characterized by the inability to open the mouth of the newborn, this can be classified according to its clinical presentation. The complications of this anomaly can be inability to protect the airway, difficulties for feeding, as well as alterations in growth. There have referred cases with different approaches, thus the therapeutic-surgical protocol will be given according to the particularities of each individual. In the present case reference is made of female infant with unilateral maxillo-mandibular-zygomatic fusion, diagnosis and follow-up


Assuntos
Humanos , Feminino , Recém-Nascido , Anormalidades Maxilomandibulares/diagnóstico por imagem , Zigoma/anormalidades , Reconstrução Mandibular/métodos , Anormalidades Maxilomandibulares/cirurgia , Zigoma/cirurgia , Impressão Tridimensional
5.
J Med Case Rep ; 10(1): 366, 2016 Dec 20.
Artigo em Inglês | MEDLINE | ID: mdl-27998317

RESUMO

BACKGROUND: Tuberculosis is considered an emerging disease worldwide; in the last 10 years, its incidence has increased to more than 9.6 million cases of active tuberculosis. In 2014, it resulted in 1.5 million patient deaths. However, oral presentation with bone involvement occurs in less than 3% of all reported cases and rarely arouses clinical suspicion on initial presentation. CASE PRESENTATION: A 15-year-old Mexican girl who had a previous diagnosis of neurofibromatosis presented to our hospital with pain and swelling in the region of the left mandibular body since November 2011. A clinical examination revealed pain in the mandibular region, a mass of soft consistency that seemed to involve bone, and a fistula with discharge of intraoral purulent material. Additionally, tachycardia and hyperthermia were observed. The left submental and submandibular regions had a 12-cm-diameter swelling, which was well-delineated and nonerythematous. The final diagnosis was established by real-time polymerase chain reaction. CONCLUSIONS: The final diagnosis of rare cases of tuberculous osteomyelitis in the jaw can be established by deoxyribonucleic acid (DNA) identification of Mycobacterium tuberculosis in the lesion. Simple and fast complementary diagnosis by real-time polymerase chain reaction is a fundamental approach to establishing early and effective pharmacological and surgical treatment.


Assuntos
Antituberculosos/uso terapêutico , Doenças Mandibulares/microbiologia , Osteotomia Mandibular , Reconstrução Mandibular , Mycobacterium tuberculosis/isolamento & purificação , Tomografia Computadorizada por Raios X , Tuberculose Osteoarticular/microbiologia , Adolescente , Feminino , Humanos , Doenças Mandibulares/diagnóstico por imagem , Doenças Mandibulares/patologia , Doenças Mandibulares/terapia , Reconstrução Mandibular/métodos , Reação em Cadeia da Polimerase em Tempo Real , Resultado do Tratamento , Tuberculose Osteoarticular/diagnóstico por imagem , Tuberculose Osteoarticular/patologia , Tuberculose Osteoarticular/terapia
6.
J Med Case Rep ; 5: 98, 2011 Mar 11.
Artigo em Inglês | MEDLINE | ID: mdl-21396085

RESUMO

BACKGROUND: Odontogenic necrotizing fasciitis of the neck is a fulminant infection of odontogenic origin that quickly spreads along the fascial planes and results in necrosis of the affected tissues. It is usually polymicrobial, occurs frequently in immunocompromised patients, and has a high mortality rate. CASE PRESENTATION: A 69-year old Mexican male had a pain in the maxillar right-canine region and a swelling of the submental and submandibular regions. Our examination revealed local pain, tachycardia, hyperthermia (39°C), and the swelling of bilateral submental and submandibular regions, which also were erythematous, hyperthermic, crepitant, and with a positive Godet sign. Mobility and third-degree caries were seen in the right mandibular canine. Bacteriological cultures isolated streptococcus pyogenes and staphylococcus aureus. The histopathological diagnosis was odontogenic necrotizing fasciitis of the submental and submandibular regions. The initial treatment was surgical debridement and the administration of antibiotics. After cultures were negative, the surgical wound was treated with a growth factor-enriched autologous plasma eight times every third day until complete healing occurred. CONCLUSIONS: The treatment with a growth factor-enriched autologous plasma caused a rapid healing of an extensive surgical wound in a patient with odontogenic necrotizing fasciitis. The benefits were rapid tissue regeneration, an aesthetic and a functional scar, and the avoidance of further surgery and possible complications.

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